Inborn Errors of Metabolism
Inborn Errors of Metabolism(先天性代谢缺陷病)
Inborn Errors of Metabolism 相关产品(95)
- GC118704-Methylumbelliferyl-β-D-GlucopyranosideCAS: 18997-57-4纯度: >99.00% / >98.00%
4-Methylumbelliferyl-β-D-Glucopyranoside是一种β-D-葡萄糖苷，可作为β-葡萄糖苷酶的荧光底物，用于检测该酶的活性。
- GC198524-Methylumbelliferyl-α-D-glucopyranosideCAS: 17833-43-1纯度: >99.00%
A fluorogenic substrate for α-glucosidase
- GC19926Methyl malonic acidCAS: 108-59-8纯度: >99.50%
A dicarboxylic acid and byproduct of propionate catabolism
- GC26265α-Hydroxyglutaric acid disodiumCAS: 40951-21-1纯度: ≥98.00%
α-Hydroxyglutaric acid (2-Hydroxyglutarate) disodium 是戊二酸的 α-羟基酸形式。
- GC405104-Methylumbelliferyl-α-D-GalactopyranosideCAS: 38597-12-5纯度: >98.00%
A fluorogenic substrate of α-galactosidase
- GC4190713C C16 Sphingomyelin (d18:1/16:0)CAS: 144236-99-7纯度: >98.00%
An internal standard for the quantification of C16 sphingomyelin
- GC420511-β-D-Glucosylsphingosine (d18:1)CAS: 52050-17-6纯度: >98.00%
A lysolipid derivative of glucocerebroside
- GC422923-Hydroxypropionic Acid (sodium salt)CAS: 6487-38-3纯度: >95.00%
A building block in the synthesis of a variety of compounds
- GC424424-Methylumbelliferyl 2-sulfamino-2-deoxy-α-D-Glucopyranoside (sodium salt)CAS: 460085-45-4纯度: >98.00%
A fluorogenic substrate of heparin sulphamidase
- GC424454-Methylumbelliferyl β-D-Galactopyranoside-6-sulfate (sodium salt)CAS: 206443-06-3纯度: >98.00%
A fluorogenic substrate of GALNS
- GC42963BODIPY-C12 Ceramide (d18:1/12:0)CAS: 1246355-58-7纯度: >98.00%
BODIPY-C12 Ceramide (d18:1/12:0)是一种荧光标记的C12神经酰胺。
- GC43035C16 Sphingomyelin (d18:1/16:0)CAS: 6254-89-3纯度: >98.00% / >99.00%
C16 Sphingomyelin (d18:1/16:0)是一种鞘磷脂形式，可变酰化位点包含palmitate (16:0)。
| 货号 | 产品名称 | CAS号 | 纯度 | 结构 |
|---|---|---|---|---|
| GC11870 | 4-Methylumbelliferyl-β-D-Glucopyranoside | 18997-57-4 | >99.00% / >98.00% | |
4-Methylumbelliferyl-β-D-Glucopyranoside是一种β-D-葡萄糖苷，可作为β-葡萄糖苷酶的荧光底物，用于检测该酶的活性。 | ||||
| GC18469 | Galactosylcerebrosides (bovine) | 85305-88-0 | >98.00% | |
A sphingolipid | ||||
| GC18609 | 1-Deoxysphinganine (m18:0) | 196497-48-0 | >98.00% / >95.00% | |
An atypical sphingolipid | ||||
| GC19852 | 4-Methylumbelliferyl-α-D-glucopyranoside | 17833-43-1 | >99.00% | |
A fluorogenic substrate for α-glucosidase | ||||
| GC19926 | Methyl malonic acid | 108-59-8 | >99.50% | |
A dicarboxylic acid and byproduct of propionate catabolism | ||||
| GC19941 | DL-Leucic Acid | 498-36-2 | ≥98% | |
| GC26265 | α-Hydroxyglutaric acid disodium | 40951-21-1 | ≥98.00% | |
α-Hydroxyglutaric acid (2-Hydroxyglutarate) disodium 是戊二酸的 α-羟基酸形式。 | ||||
| GC40016 | Ganglioside GM2 Mixture (sodium salt) | 19600-01-2 | >98.00% | |
A mixture of ganglioside G M2 | ||||
| GC40041 | Cholesteryl Lignocerate | 73024-96-1 | >98.00% | |
A cholesterol ester | ||||
| GC40341 | Tetrahydro-11-deoxy Cortisol | 68-60-0 | >95.00% | |
A metabolite of 11-deoxycortisol | ||||
| GC40510 | 4-Methylumbelliferyl-α-D-Galactopyranoside | 38597-12-5 | >98.00% | |
A fluorogenic substrate of α-galactosidase | ||||
| GC41582 | 4(Z),7(Z)-Decadienoic Acid | 169392-17-0 | >98.00% | |
A PUFA | ||||
| GC41614 | 24-dehydro Cholesterol | 313-04-2 | >98.00% | |
An immediate precursor of cholesterol | ||||
| GC41907 | 13C C16 Sphingomyelin (d18:1/16:0) | 144236-99-7 | >98.00% | |
An internal standard for the quantification of C16 sphingomyelin | ||||
| GC42051 | 1-β-D-Glucosylsphingosine (d18:1) | 52050-17-6 | >98.00% | |
A lysolipid derivative of glucocerebroside | ||||
| GC42292 | 3-Hydroxypropionic Acid (sodium salt) | 6487-38-3 | >95.00% | |
A building block in the synthesis of a variety of compounds | ||||
| GC42442 | 4-Methylumbelliferyl 2-sulfamino-2-deoxy-α-D-Glucopyranoside (sodium salt) | 460085-45-4 | >98.00% | |
A fluorogenic substrate of heparin sulphamidase | ||||
| GC42445 | 4-Methylumbelliferyl β-D-Galactopyranoside-6-sulfate (sodium salt) | 206443-06-3 | >98.00% | |
A fluorogenic substrate of GALNS | ||||
| GC42695 | Acetoacetyl Coenzyme A (sodium salt hydrate) | - | >98.00% / >99.50% | |
A precursor to HMG-CoA | ||||
| GC42963 | BODIPY-C12 Ceramide (d18:1/12:0) | 1246355-58-7 | >98.00% | |
BODIPY-C12 Ceramide (d18:1/12:0)是一种荧光标记的C12神经酰胺。 | ||||
| GC43006 | C12 Ceramide (d18:1/12:0) | 74713-60-3 | >98.00% | |
A naturally occurring ceramide | ||||
| GC43032 | C16 Globotriaosylceramide (d18:1/16:0) | 137896-85-6 | >98.00% | |
A sphingolipid | ||||
| GC43033 | C16 Lactosylceramide (d18:1/16:0) | 4201-62-1 | >98.00% | |
A bioactive sphingolipid | ||||
| GC43035 | C16 Sphingomyelin (d18:1/16:0) | 6254-89-3 | >98.00% / >99.00% | |
C16 Sphingomyelin (d18:1/16:0)是一种鞘磷脂形式，可变酰化位点包含palmitate (16:0)。 | ||||