Inborn Errors of Metabolism
Inborn Errors of Metabolism(先天性代谢缺陷病)
Inborn Errors of Metabolism 相关产品(95)
- GC49388N-Butyldeoxynojirimycin-d9 (hydrochloride)CAS: 1883545-57-0纯度: >99.00%
An internal standard for the quantification of N-butyldeoxynojirimycin
- GC49472Methylmalonic Acid-d3CAS: 42522-59-8纯度: >99.00%
An internal standard for the quantification of methylmalonic acid
- GC49479Hypoxanthine-d4CAS: 2483831-32-7纯度: >99.00%
An internal standard for the quantification of hypoxanthine
- GC49782L-Phenylalanine-13C6CAS: 180268-82-0纯度: >99.00%
An internal standard for the quantification of phenylalanine
- GC52009Isovaleryl-DL-carnitine-d9 (chloride)CAS: 2608872-54-2纯度: >99.00%
An internal standard for the quantification of isovaleryl-DL-carnitine
- GC5208321-DeoxycortisoneCAS: 1882-82-2纯度: >95.00%
A corticosteroid metabolite of 11-keto progesterone
- GC521222’-Deoxyadenosine-5’-diphosphate (sodium salt)CAS: 402491-35-4纯度: >95.00%
A nucleotide diphosphate
- GC52231Heptadecanoyl-L-carnitine-d3 (chloride)纯度: >95.00%
An internal standard for the quantification of heptadecanoyl-L-carnitine
- GC52323L-Isoleucine-13C6CAS: 201740-82-1纯度: >95.00%
An internal standard for the quantification of L-isoleucine
- GC52404γ-Glu-Phe (trifluoroacetate salt)纯度: >98.00%
A dipeptide with metabolism-altering activity
| 货号 | 产品名称 | CAS号 | 纯度 | 结构 |
|---|---|---|---|---|
| GC49240 | N-Propionylglycine | 21709-90-0 | >98.00% | |
A glycine-conjugated form of propionic acid | ||||
| GC49246 | N-(3-Phenylpropionyl)glycine | 56613-60-6 | >98.00% | |
An acylglycine | ||||
| GC49323 | Norcholic Acid | 60696-62-0 | >95.00% | |
A bile acid and derivative of cholic acid | ||||
| GC49325 | Dihydroxyacetone Phosphate (magnesium salt hydrate) | - | >95.00% | |
甘油脂前体 | ||||
| GC49328 | UDP-α-D-Galactose (sodium salt) | 137868-52-1 | >98.00% | |
A nucleotide sugar | ||||
| GC49388 | N-Butyldeoxynojirimycin-d9 (hydrochloride) | 1883545-57-0 | >99.00% | |
An internal standard for the quantification of N-butyldeoxynojirimycin | ||||
| GC49472 | Methylmalonic Acid-d3 | 42522-59-8 | >99.00% | |
An internal standard for the quantification of methylmalonic acid | ||||
| GC49479 | Hypoxanthine-d4 | 2483831-32-7 | >99.00% | |
An internal standard for the quantification of hypoxanthine | ||||
| GC49499 | 5(Z)-Dodecenoic Acid | 2430-94-6 | >99.00% / >98.00% | |
A medium-chain unsaturated fatty acid | ||||
| GC49782 | L-Phenylalanine-13C6 | 180268-82-0 | >99.00% | |
An internal standard for the quantification of phenylalanine | ||||
| GC49840 | 2-Methylbutyrylglycine | 52320-67-9 | >95.00% | |
A metabolite of isoleucine | ||||
| GC52009 | Isovaleryl-DL-carnitine-d9 (chloride) | 2608872-54-2 | >99.00% | |
An internal standard for the quantification of isovaleryl-DL-carnitine | ||||
| GC52083 | 21-Deoxycortisone | 1882-82-2 | >95.00% | |
A corticosteroid metabolite of 11-keto progesterone | ||||
| GC52122 | 2’-Deoxyadenosine-5’-diphosphate (sodium salt) | 402491-35-4 | >95.00% | |
A nucleotide diphosphate | ||||
| GC52219 | Heptadecanoyl-L-carnitine (chloride) | 173686-69-6 | >95.00% | |
A long-chain acylcarnitine | ||||
| GC52231 | Heptadecanoyl-L-carnitine-d3 (chloride) | - | >95.00% | |
An internal standard for the quantification of heptadecanoyl-L-carnitine | ||||
| GC52323 | L-Isoleucine-13C6 | 201740-82-1 | >95.00% | |
An internal standard for the quantification of L-isoleucine | ||||
| GC52404 | γ-Glu-Phe (trifluoroacetate salt) | - | >98.00% | |
A dipeptide with metabolism-altering activity | ||||
| GC52491 | Globotriaosylceramide (non-hydroxy) (porcine RBC) | - | >98.00% | |
A sphingolipid | ||||
| GC52492 | Globotriaosylceramide (hydroxy) (porcine RBC) | - | >98.00% | |
A sphingolipid | ||||
| GC52493 | Glucosylceramide (bovine buttermilk) | - | >98.00% | |
A sphingolipid | ||||
| GC52496 | Sulfatide (bovine) (sodium salt) | - | >95.00% | |
A mixture of isolated bovine sulfatides | ||||
| GC91083 | Tiopronin-Cysteine Disulfide | 77591-18-5 | >95.00% | |
一种硫普罗宁的代谢产物。 | ||||